DCH – Sept 2005

 

Paper I  Question 2

 

a)       Describe the diagnosis and management of gastroesophageal reflux disease in children (GERD)

 

Symptoms and signs of GERD

Typical

  • Excessive regurgitation/vomiting
  • Weight loss/Failure to thrive
  • Irritability with feeds/Food refusal
  • Dysphagia
  • Chest/epigastric discomfort
  • Excessive hiccups
  • Haematemesis/Anaemia
  • Aspiration pneumonia
  • Esophageal obstruction due to stricture

Atypical

  • Wheeze/intractable asthma
  • Cough/stridor
  • Apnoe/Apparent life-threatening events
  • Cyanotic episodes
  • Sleep disturbance
  • Generalized irritability
  • Neuro-behavioural symptoms

 

Investigation of GERD

  • 24-hour esophageal pH study
  • Barium radiology
  • Alkaline reflux
  • Isotope studies ‘milk scan’
  • Esophagoscopy, esophageal biopsy

 

Primary care management includes parent education regarding dietary modifications, avoidance of smoke exposure and of unnecessary seated and supine positioning. It may be useful to observe a feeding of an infant in order to offer focused assistance with feeding and/or positioning. If symptoms are not relieved consider a 2-week trial of and elemental formula to assess possible cow milk intolerance. Breastfeeding mothers may try eliminating cow milk protein from her diet for a similar period.

Infants with GERD benefit from prone and left lateral positions for the postural management. Cautions about avoiding soft bedding materials must be given with any recommendations for prone positioning.

Feeding suggestions:

  • Encourage breast feeding or breast milk
  • Give small, more frequent feedings, allow extra time to burp as needed
  • Try thickening milk/formula
  • Introduce solids when developmentally appropriate

 

Medical treatment of GERD includes: antacids, thickeners, H2 blockers, prokinetics.   Confirm GERD and to rule out obstruction before initiating motility agents.

Consider consultation/referral for further evaluation if:

  • Symptoms fail to resolve with conservative management
  • Evaluation for GERD beyond barium radiography is required
  • If symptoms attributed to reflux persist beyond 1 year of age
  •  

Surgical treatment: fundoplication, pyloroplasty, gastrostomy.

 

b) i) The criteria for diagnosis of Kawasaki disease

 

·         Fever lasting at least 5 days

·         Presence of 4 out of the following 5 clinical signs not explained by other known disease process.

1.  Swelling and erythema of hands and feet (acute phase) or 

     periungual  desquamation (convalesent phase)

2.        Mucosal changes of the oropharynx (injected pharynx, red or

      dry fissured lips, strawberry tongue)

                  3.  Cervical lymphadenopathy: anterior cervical lymph note at least 1.5 

                       cm in diameter

4.        Bilateral non-purulent conjunctivitis

5.        Diffuse polymorphous rash, primarily truncal, nonvesicular

These criteria may not all occur simultaneously.

 

b) ii) Takayasu’s arteritis (TA)

            

TA is the third most common form of childhood vasculitis. The cause of TA remains unknown, although histopathology and immunohistochemistry of biopsy samples suggest a primarily T-cell-mediated mechanism. Pathologically TA lesions consist of granulomatous changes progressing from the vascular adventia to the media.

 

The diagnosis of TA is based on the distribution of involvement-primarily the aorta and its branches-and the young age of patients, typically under 40 years. Onset of TA is most commonly during the third decade of life, but childhood disease has been reported as early as the first year of life. There is significant preponderance of female patients.

 

Signs and symptoms: hypertension, cardiomegaly, fever, fatigue, palpitations, nodules, abdominal pain, arthralgia, claudication, weight loss, and chest pain.

Delayed diagnosis is the cause of high mortality in children.

 

Diagnostic methods: agniography, and less invasive - CT / MRI angiography are the standard methods.

 

Laboratory tests: WBC, ESR, CRP can be normal despite ongoing inflammation.

 

Early diagnosis and aggressive therapy are important to prevent irreversible vessel damage. Steroid and the immunosuppressive agents (cycophosphamide, methotrexate,  azathiprine) have shown variable efficacy. Before starting such treatment it is important to test patients for tuberculosis because aortitis can be associated with mycobacterial infection.

 

c)  Discuss the causes, pathophysiology and management of hypocalcaemia in children

Extracellural calcium levels are maintained at 2.2 – 2,6 mmol/l.

Ionized Ca is a better measure then total Ca. Consider values <1.1 mmol as low.

For total Ca low values <2,2 mmol  in children and <2.0 mmol in term infants.

 

Calcium regulation is maintained by parathyroid hormone (PTH), vitamin D, and calcitonin through complex feedback loops. These compounds act primarily at bone, renal and GI sites. Calcium also is affected by magnesium and phosphorus.

Deficiency or  impairment function of one of the three main determinants of circulating calcium can lead to hypocalcaemia.

 

The main causes of hypocalcaemia include:

·         Vitamin D deficiency, resistance/impaired metabolism

·         Dietary calcium deficiency

·         Malabsorption states

·         Hypomagnesaemia, hyperphosphataemia, hypoalbuminaemia

·         PTH deficiency or resistance

·         Renal/hepatic failure

·         Acute pancreatitis, sepsis, malignancy.

·         Blood transfusion

·         Prematurity, asphyxia, neonate of diabetic mother

·         Drug therapy (anticonvulsants)

 

Management:

  • Treat the underlying disease
  • Acute symptomatic:  1-2 ml/kg/dose of 10% Ca gluconate IV over 20 min. preferably with ECG control. If no response , give 0.1 ml/kg of 50% Mg sulphate IM/slow IV. Beware of hyperphosphataemia in Chronic Renal Failure
  • Chronic: oral supplements of calcium 

 

d) Describe your approach to a previously well 2-year-old child who presents with vomiting for two days.

 

Nausea and vomiting are common sequelae of a multitude of disorders that can range from mild, self-limited illnesses to severe, life-threatening conditions.

A standardized approach to children with nausea and vomiting cannot be recommended since many pathologic states involving several systems (including gastrointestinal, respiratory, neurologic, renal) may be responsible. Younger children may not be able to describe nausea, which may further complicate diagnosis. The best course of action should be dictated by the medical history, taking into consideration clinical features of specific disorders and their relative frequency among children in different age groups. The most important consideration during the initial encounter is recognition of serious conditions (such as intestinal obstruction and increased intracranial pressure) for which immediate intervention is required.

 

Evaluate the child with a careful history and physical examination. The goals are to identify any acute needs the child may have: to quantify the degree of dehydration and to assess the need for further testing. There is limited value in screening laboratory tests, as the majority of children with vomiting have uncomplicated GE or URI. Although some well-defined clinical pictures demand urgent radiologic/laboratory workup (e.g. bilious vomiting, suspected intussusception or menitngitis) 

 

The differential diagnosis for vomiting is influenced by the age of the patient.

 

Common causes of vomiting in a 2-year old child are: gastroenteritis, pneumonia, URI, OM, UTI, meningitis, toxin/drugs ingestion. Life –threatening causes: appendicitis, intussusception, diabetic ketoacidosis,  toxic ingestion, meningitis, incarcerated hernia, and ileus.

 

Clinical clues can be obtained from the appearance of the vomitus.

Appearance – Source/Cause:

·         Undigested food – Reflux

·         Digested food – Stomach, proximal to pylorus

·         Yellow-gree, bilious – Obstruction distal to ampulla of Vater or retrograde peristalsis

·         Feculent – Distal obstruction, colonic stasis

·         Blood,  bright red – Esophagus or stomach above the cardia with minimal contact of blood with gastric secretion. Blood, brown, “coffee grounds” – Gastric bleeding 

 

Management

·         Treat dehydration or maintain adequate hydration

·         Provide treatment for specific cause of vomiting

·         Antiemetics are not advised

 

Treatment for vomiting includes: drinking gradually larger amounts of clear liquids; avoiding solid food until the vomiting episode has passed; resting; and temporarily discontinuing all oral medications, which can irritate the stomach and make vomiting worse. If vomiting last more than 24 hours, an oral rehydrating solution should be used to prevent and treat dehydration.

 

 

Paper 1 Question 4

 

a) Describe how you would manage a known asthmatic who presents with an acute severe exacerbation.

 

b) Describe your approach to the management and subsequent follow up of a 6 week old boy with a proven urinary tract infection

 

c) Describe the criteria for diagnosing a simple febrile seizure, the acute management, and the advice you would give the parents of a 2 year old child with a recent simple febrile seizure including advice regarding prognosis.

d) Discuss your approach to a well 6 week old child that presents with a persistent conjugated hyperbilirubinaemia

 

a)Initial assessment and treatment:

  • Inhaled short acting Beta-2 agonist(nebulized oe MDI) , repeat dose every 10-20min
  • Oxygen
  • Consider inhaled ipratropium bromide added to nebuliser
  • Systemic corticosteroids: prednisone

Clinical assessment:look for danger signs/severe episode:

  • Previous ICU admission
  • Duration of acute episode>12hrs
  • Recent course of oral steroids
  • Drowsy or confused
  • Silent chest on auscultation
  • Oxygen sats<95%
  • PEFR<60% expected
  • Severe retraction/use of accessory muscles

THEN:

Ř        continuous inhaled Beta-2 agonists

Ř       Ivi corticosteroid: dexamethasone

Ř       Stat dose ivi B2 agonists(ventolin)

Ř       Adrenaline subcut if moribund

Ř       Hydrate if dehydrated

 

REASSESS:

·         Good response: continue inhaled B2 agonists/maintenance Rx, complete course of oral steroids, follow up plan

·         Incomplete response: admit to ward, hourly B2 agonist+inhaled ipratropium, oxygen, oral steroid

·         Poor response with ongoing severe retraction/silent chest/altered LOC/hypoxia/PEFR<30%: refer/admit ICU

 

ON DISCHARGE:

  • Review of medication/inhaler technique/appropriateness, precipitant etc with education

 

b)

  • Confirm meets criteria for UTI and that sterile specimen sent originally(CSU/SPA)
  • In patient systemic antibiotic treatment with cephalosporin for 1week to 10 days, monitoring urine output, stream etc
  • Good history on any family history renal problems, any abnormality on antenatal ultrasound, stream
  • Thorough examination including blood pressure, feel for abdominal masses, enlarged kidneys to suggest hydronephrosis, palpable bladder suggesting trabeculation from PUVs
  • Ultrasound KUB whilst inpatient to exclude underlying abnormality, manage/refer accordingly
  • Discharge on prophylactic antibiotics: augmentin/cefuroxime
  • MCUG as outpatient in 3-6 weeks time
  • Follow-up
  • Counsel mum that if child febrile in future to always get nurse/Dr to check urine

 

 

c)

Diagnosis

  • age 6months-5yrs
  • Extracranial febrile illness
  • Often at onset of illness
  • Generalized
  • Lasts less than 15min
  • Once, in early phase of illness
  • No neurological abnormalities on recovery

 

Management

  • ABC
  • Reduce temp: remove clothes, tepid sponge, paracetamol
  • Rectal diazepam to terminate seizure
  • Check blood glucose
  • Look for source of infection: clinical exam, ENT,urine dipstix,LP if <18months/2years

 

 

Advice/Prognosis

  • 40% have second febrile fit with subsequent febrile illness
  • excellent prognosis, no risk intellectual impairment or epilepsy if simple
  • antipyretics and tepid sponging with subsequent febrile illnesses
  • if fits, put on side, prevent aspiration
  • take to clinic/Dr if lasts>5-10min

 

d)Need to define whether there is complete obstruction/extrahepatic obstruction

  • History: pale stools/dark urine suggests complete obstruction, but always do own “bakkie tests” and look at stool, if cut surface pale indicates complete obstruction and need for urgent referral to secondary or tertiary centre to exclude biliary atresia
  • Other information on History: when did jaundice start, (birth or later), VDRL status of mother, any other illnesses(especially viral) during pregnancy, family history, prematurity/ICU/TPN
  • Examination: dysmorphism(Alagilles), rashes(syphilis, CMV), odour, microcephaly(CMV), hepatosplenomegaly etc

 

  • Baseline investigations:
    • (If child unwell: full workup for sepsis) but question says “well”
    • Urine dipstix.MC&S: must exclude UTI as cause
    • Liver function(enzymes, albumin, coag)+FBC
    • VDRL, TORCH Screen, HepB and C
    • Urine reducing substances(galactossaemia)
    • Thyroid function
    • Ultrasound

·         Further investigation/management depending on cause

·         Complete obstruction/cannot define/metabolic: refer (for cholangiogram etc)

·         Rx congenital syphilis etc

 

 

 

Paper 1 Question 5

 

Management of Attention Deficit and Hyperactivity Disorder

 

1. Evaluate children/adolescents suspected of having ADHD based on DSM-IV diagnostic criteria using consistent and appropriate diagnostic tools.

·         Although the core symptoms of inattention, impulsivity and hyperactivity are characteristic, their severity and pattern are highly variable across individuals.

·         The evaluation of primary symptoms should include information from multiple sources such as parents, the child, and school personnel.

·         There is no single evaluation tool available to make a definitive diagnosis of ADHD.

·         Screen all patients for other primary conditions or comorbidities and appropriately refer to subspecialty consultation for further evaluation.

·         Many children can exhibit symptoms of ADHD at some point in their development, but it is important to note that common symptoms (inattention, hyperactivity, disruptive behavior, academic difficulty), can be caused by a number of other difficulties. At this stage of the process, the clinician must consider diagnoses other than ADHD.

 

2. Coordinate a simultaneous multimodal management plan that involves parent, child, and school-focused interventions.

 

3. Establish communication and intervention linkages with related systems (e.g. schools, mental health, etc

 

4. Establish appropriate use of psychostimulants in both initial and ongoing management of patients with ADHD.

Psychostimulant medications are considered first-line therapy in children with ADHD: these include psychostimulant medications such as methylphenidate.

 

5. Provide consistent and comprehensive monitoring and care coordination for all patients with ADHD including pharmacologic and non-pharmacologic interventions, identification and management of emerging comorbidities, and the impact of ADHD condition on patients, their families, and schools.

 

 

Congenital Hip Dislocation

 

Epidemiology

·         Congenital hip dislocation (CHD) occurs more commonly in girls than in boys.

·         The left hip is twice as often involved as the right and bilateral dislocation occurs in more than 25 percent of affected children.

·         Congenital hip dislocation is more frequently encountered in Whites than in Blacks

Clinical Presentation:
In the neonate the diagnosis may be made clinically because the femoral heads are not ossified yet. The Ortolani/Barlow manoeuvre is used in which you attempt dislocation of the flexed hip by abduction of the proximal femur producing a click on posterior dislocation and another as the femoral head slides back into the acetabulum with adduction.

  • Ortolani's "jerk" sign ("clunk of entry" or reduction sign);
  • Barlow's test ("clunk of exit" or dislocation sign);
  • Telescoping or pistoning action of thighs, due to lack of containment of femoral head with acetabulum;

 

Etiology/Pathophysiology:
In utero dislocation of hip is unusual. Most dislocations occur after birth and are related to unstable or dislocatable hips.

  • Congenital hip dislocation is often the only birth defect a child has.
  • It is believed that most congenital hip dislocations occur due to a combination of environmental and genetic factors.
  • Major etiologic factors are ligamentous laxity of the joint capsule and intrauterine (breech) presentation.
  • Parents of a child with congenital hip dislocation have about a 6% chance of having another child with congenital hip dislocation.

Imaging Findings:
Ultrasound of the hips is very useful in making the diagnosis in the newborn.

Femoral head ossification centers appear at 3-6 months so radiographs are not useful in the newborn. By 2-4 months old you begin to see lateral displacement of the femur and an increased acetabular angle.

 

Treatment

Ninety percent of dislocatable hips will stabilize in first 2 months of life if not treated, but the ones which will stabilize cannot be predicted so all patients are treated with a flexion-abduction-external rotation device.

The principal treatment for CHD is conservative, especially if diagnosed early. The most common technique is to reduce the dislocation of the femoral head by means of a flexion/abduction maneuver, for a sufficient period of time to permit proper growth of the head and acetabulum, which in turn assures a congruent and stable hip joint. This technique is usually performed on children in the very early stages of CHD and in infants under two years of age; which include splinting, with a Frejka splint or Pavlik harness.

If the conservative approach fails, or the child is too old, or the deformities are too advanced, surgical management is indicated.

The key to preventing significant deformities and future arthrosis of the hip is to diagnose CHD early, before the child begins to walk, when conservative care is most effective, and before the femoral head has completely ossified.

 

Safety advice to parents, older children or local authorities to prevent children getting involved in road traffic accidents.

 

Parents/older children

Bicycle helmets

Car safety seats

Seat belts

Visibility – reflective material

Advice on crossing roads

Dangers of drunk driving (adoslescents)

 

Local Council

Pedestrian crossings

Scholar patrols

Street lighting

Pavements

Play areas (parks) – not streets

Speed humps – traffic calming

Education – by parents, schools and authorities

Legislation – fines

 

SIDS counselling

Most parents who have lost an infant to SIDS are grief-stricken and unprepared for the tragedy. They usually feel guilty. They may be further traumatized by investigations conducted by police, social workers, or others.

Counselling and support from specially trained doctors and nurses and other parents who have lost an infant to SIDS are critical to helping parents cope with the tragedy. Specialists can recommend reading materials, web sites, and support groups to assist parents.

At the time, parents need empathy and support, e.g. in some cultures it may be appropriate to hold their baby one last time before the body is sent to the mortuary.

Delay discussion of SIDS avoidance measures to a subsequent visit (in 4-6 weeks time when the autopsy results are available) as it is inappropriate to do this now.

 

An autopsy is needed. Autopsies indicate a definite explanation in about 20% of cases of sudden infant death. In addition, an autopsy can often put to rest any doubts the parents may have

 

 

Paper 2 Question 1

 

Mpho, a 12 week old female infant, is brought to the well baby clinic.  She was born at 34 weeks gestation.  Her mother is HIV positive, but Mpho is clinically well and thriving.  Mpho received all her vaccines at birth, but none since. Her mother was advised by a nurse to delay immunisation until Mpho reached 6 weeks corrected age.  The clinic sister is unsure whether to immunise Mpho as she has a runny nose, cough and a temperature of 38.1oC. The sister is also concerned about giving oral polio drops to Mpho because of her mother’s HIV status.

 

a) Explain whether each of the following are valid contraindications to immunisation:                                                                                                                      (3)

 

  1. Upper respiratory infection

No. A common infection that does not intefere with immune response.

               

  1. Fever of 38.1oC                    

No. Only a fever >38.5° would be a relative contra-indication

 

  1. Treatment with antibiotics                 

No. Antibiotics do not interfere with the immune response.               

 

b) Was the nurse’s advice to postpone immunisation to six week’s corrected age appropriate?                                                                                                                                          (1)

No. Pre-term infants should be immunized at the appropriate chronological age with the full dose of vaccine.                                                                                                                                

c) What are current recommendations about immunising HIV-exposed and -infected children?                                                                                                                           (3)

 

WHO guidelines for immunizing children with HIV infection and infants born to HIV-infected women differ only slightly from the general guidelines.

HIV-infected children should receive all EPI vaccines, including live vaccines

BCG and yellow fever vaccines should be withheld from symptomatic HIV-infected children.

The benefits of measles and poliovirus vaccines far outweigh the potential risks in HIV-infected children.

Only one serious complication (fatal pneumonia) has been attributed to measles vaccine administered to a severely immunocompromised adult. An extra dose of measles vaccine is recommended at 6 months of age in order to provide protection at a younger age than for non-HIV-infected infants and to improve protection against measles.

Although two HIV-infected infants have developed vaccine-associated paralytic poliomyelitis, several million infected children have been vaccinated and the evidence does not suggest that there is an increased risk.

 

d) Comment on the efficacy of vaccines offered to HIV infected children. (3)

Response to most EPI vaccines is adequate (though may be less efficacious than in immunocompromised children)

HIV-infected children and adults develop lower geometric mean antitoxin titres and are more likely than uninfected persons to lose antibody within a few years after vaccination. Some studies have correlated antibody titres with CD4+ T-lymphocyte counts

Efficacy of congugated vaccines is reduced (by about half)

               

e) List two common adverse reactions that occur after DTP immunisation? (2)

Many children experience adverse reactions within 48 hours after the DTP immunisation, including pyrexia (>38.5oC), local induration and tenderness. This may manifest as screaming.   

 

f) How may a caregiver prevent or reduce these adverse events?              (1)

By giving paracetamol ˝ hour before and regularly (3-4 hourly) after the vaccination

                       

g) List two absolute contraindications to continuing DTP immunisation.  (2)

Convulsions, encephalitis, focal neurological signs and collapse with shock, anaphylactic reaction.

 

Mpho’s mother is concerned about the possible adverse events related to DPT vaccine. She asks you about the possible benefits of using another vaccine type. She read in the “Mother and Baby” magazine about an acellular pertussis vaccine, and asks whether this vaccine may not be preferable. You agree to investigate this option. You find the following abstract on a Medline search

 

A trial of three-component, and five-component acellular pertussis vaccines compared with whole-cell pertussis vaccine.

BACKGROUND: Trials in
Italy and Sweden showed high efficacy for three-component and five-component acellular pertussis vaccines, and poor efficacy for a whole-cell vaccine. We compared the efficacy of two acellular vaccines with a whole-cell vaccine.

METHODS: We enrolled 62 195 babies aged 2-3 months. Babies were vaccinated at age 3 months, 5 months and 12 months. They were randomly assigned a three-component acellular DTP vaccine (n = 20,728), a five-component acellular DTP vaccine (n = 20,747), or a whole-cell DTP vaccine (n = 20,720).

We collected data for all reported cases of culture-confirmed pertussis during 3 years of follow-up. Analyses were by intention to treat.

FINDINGS: For culture-confirmed pertussis, there were 19 cases in the whole-cell group (relative risk 1.00), compared with 27 in the five-component group (relative risk 1.40 [0.78-2.52]), and 49 in the three-component group (relative risk 2.55 [1.50-4.33]). Hypotonic hyporesponsiveness occurred significantly more frequently in the whole-cell group (p < 0.05) and was more frequent in the acellular groups than previously reported. High fever and seizures occurred more frequently after whole-cell vaccine than after any of the acellular vaccines (p < 0.001).

 

h) What study design was used in this trial?                                                  (1)

Randomised controlled trial

 

i) What was the primary study outcome?                                                                        (1)

Cases of culture-confirmed pertussis

 

j) What is meant by an intention to treat analysis?                                        (1)

Study participants are analysed at the end of a trial in the group they were initially assigned to, rather than on what treatment they actually received.

 

k)       Was there a significant difference in the number of culture confirmed pertussis cases between those who were given whole cell vaccine and:

i.         those given 5-component acellular vaccine? Explain                             (1)

No, relative risk was 1.40 [0.78-2.52]. The 95% confidence interval includes 1.

 

ii. those given three component acellular vaccine? Explain          (1)

Yes, relative risk was 2.55 [1.50-4.33]. The 95% confidence interval exceeds 1. (At higher risk)

 

l) What will you advice Mpho’s mother based on this trial? Explain your choice (2)

She should use the 5-component acellular pertussis vaccine (if available), because it is as efficacious as the whole cell vaccine in preventing culture-proven pertussis, and has fewer adverse effects.

                                                                                                                                                               

m) Explain what is meant by a “conjugated” vaccine and why they are more immunogenic than “ordinary” vaccines ?                                                                  (2)

Combining a polysaccharide (bacterial Ag) to a protein carrier increases the antigenicity of a vaccine. Because many purified polysaccharides are T-independent antigens, vaccines composed of these antigens are often ineffective in infants and young children younger than 2 years of age. However, by conjugation to a protein carrier, a polysaccharide can acquire the antigenic properties of the protein and resulting characteristics of a T-dependent antigen, including immunogenicity in infants. This phenomenon is the basis of the development of the new Hib and pneumococcal conjugate vaccines.

 

n) Explain the difference between passive and active immunisation? (2)

Active- depends on an individual to mount an immune response

Passive- depends on antibodies (or immunity) produced by another individual, including an infant’s mother.

 

p) Briefly discuss the benefits (if any) of passive vaccination in the following situations                                                                                                                                     (8)

                i) A 12 year old boy with tetanus

Tetanus immunoglobulin (TIG) should be used for passive protection of individuals who have sustained a tetanus-prone wound, where the person has not received three or more doses of a tetanus toxoid-containing vaccine or where there is doubt about their tetanus vaccination status. It should be given as soon as practicable after the injury.

 

                ii) A neonate born to a mother with chicken pox

High-titre varicella-zoster immunoglobulin (ZIG) is available on a restricted basis for the prevention of varicella in high-risk subjects. ZIG must be given early in

the incubation period (within 96 hours of exposure). Normal immunoglobulin (human) can be used for the prevention of varicella if ZIG is unavailable.

               

iii) A child attending a creche where another child has been diagnosed as having hepatits A

A single case of hepatitis A probably does not justify the mass

use of normal human immunoglobulin (NIGH). Two or more cases (associated with a day-care or pre-school facility) that occur in different households is strongly suggestive that transmission of hepatitis A is occurring within the facility. NIGH should then be offered to all staff and attendee children at the facility.

 

                iv) An child with leukemia residing in a ward with a suspected case of measles

Measles immune globulin (MIG) or normal immunoglobulin (human) should be considered for immunocompromised contacts of patients with confirmed or suspected measles. If immunoglobulin is administered within 7 days of exposure, it can prevent or modify measles in non-immune persons.

 

q) What advice would you provide to a parent who refuses immunisation because:

                                                                                                                                                                (6)

i) She believes in homeopathy

                Homeopathy is not a contra-indication

                Homeopathy cannot protect from infections

Important bodies, such as London School of Hemeopathy, recommend vaccination

 

             ii) She is concerned about the association of the measles vaccine with autism

             First proposed by Wakefield in 1999 (small study [20 children] that was flawed)   

Various studies (involving many thousands of children) have since examined the association, and none have established any association.

                                                                                                                                               

 

 

Paper 2; Question 2

 

A 24 year unbooked mother has just delivered a 33 week premature baby at the hospital where you are the medical officer on call.  Birth weight is 1.2 kg.  The baby has Apgar scores of 8 and 10, looks pink in room air and has a respiratory rate of 60 breaths per minute.

 

a)             Initial Management

 

§         Keep warm – incubator or overhead heater. 

§         Examination. 

§         Give oxygen.

§         IVI fluids 60 ml/kg. 

§         Oral feeding if remains stable after 24-48 hours. 

§         Monitor dextrostix. 

§         Theophylline for apnoea prophylaxis. 

§         ±Antibiotics-gram + and – cover. 

§         Check maternal blood group, WR, VCT

 

b)            Repeated Apnoeanic Attacks – most likely causes

 

§         Apnoea of prematurity infections – septicaemia, meningitis, NEC, aspiration pneumonia.

§         Metabolic/endocrine abnormalities – Na, calcium glucose.

§         Anaemia/Polycythamia

§         Congenital heart dx – PDA

§         Temperature control ↑ or ↓. Hypoxia. IVH

 

Investigations: Septic screen

 

§         FBC, U&E, calcium, blood and urine cultures, LP, CXR + Abdominal X-ray, head sonar

 

        Management

 

§         Antibiotics, feeding if no features of NEC, theophylline, ±blood transfusion

§         Apnoea monitor, ventilation of apnoea persists.

 

c)             Supportive treatment and Supplements in Ward

 

§         Feeding – gradual ↑ oral feeds.  1st NG feeding, volume 60ml/kg – 150ml/kg

§         Cup feeding if on formula or breast feeding

§         Temperature control – incubator then KMC

§         Theophylline for apnoea of prematurity prophylaxis

§         Supplements – vitamin K on day 1, vidyalin or MVT or vitamin B co-syrup, vitamin D, sunflower oil or polycose, iron after 3 weeks.

 

d)            Discharge criteria and arrangements for follow-up

 

§         Full oral feeding – breast feeding or formula

§         Adequate weight gain (1.7 – 2.0kg)

§         Thermally stable – can be send home on KMC position.  Can use KMC score sheet.

§         Vaccination – BCG + OPV

 

Follow-up six weeks or earlier – check weight gain, neurological function, cardiac defects, eye examination.

Advise to go for six weeks vaccines.

 

 

Paper 2;Question 3:

 

A 4-year old girl presents to you with a vaginal discharge for 2 days. The mother says that the discharge is greenish and quite copious. Just before this started, she noticed a spot of dry blood on the child’s panty, but she did not really take notice because she was on her way to work. Since then the child did not want her to wash her genital area and she complained about when she had to urinate. When the discharge started, the mother became concerned, but because she works night shifts, this was her first opportunity to bring the child to the doctor.

 

a)       What is the differential diagnosis for a 4-year old child with a vaginal discharge? (5)

Worm infestation – Enterobius vermicularis; Bubble baths and nylon/synthetic panties; Sexually transmitted infections due to CSA; Local infection due to injury – also CSA; Foreign object in vagina; Poor hygiene with secondary infection, (and some other RARE conditions for half the mark).

b)       You suspect from the history that the child has been sexually abused. Briefly describe all the responsibilities of the doctor in the management of child sexual abuse. (10)

Take a full history (if possible, no detail about CSA)
Full examination of the child (growth parameters, sexual development -Tanner scale, etc.)
Collect medico-legal evidence
Further investigations as indicated: for physical abuse, pregnancy test, syphilis & HIV tests
Explain findings to parent (&child)
Team – approach
Write notes, reports, J88 forms
Safety of the child – ensure but not arrange
Treatment where indicated
Referral & follow-up

 

c)       What special investigations would you do in this case (5)

Vaginal MCS swab, wet smear, chlamydiae test; HIV, RPR, urine MCS, forensic swabs and tests if <72 hours.

d)       If the child had presented 3 days before, when the mother noticed the blood on the panty, and on examination CSA was suspected, would HIV post-exposure prophylaxis been indicated? What is the rationale behind HIV PEP for child sexual abuse cases and describe the process you would follow when providing PEP.(10)


(This is the complete answer, but for points, the basics)

All parents/guardians of children under the age of 14 years, presenting to a health facility after being sexually abused should be counselled by the examining health worker about the potential risk of HIV transmission.

If the child presents within 72 hours of being sexually abused, antiretroviral drugs [AZT (zidovudine) and 3TC (lamivudine), or Combivir (AZT/3TC combination) plus Kaletra (lopinavir/ritonavir combination] should be offered to prevent HIV transmission.

The following points should be covered in the counselling:

o        The risk of transmission is not known.

o        There is strong evidence to support the use of a combination of antiretroviral drugs in preventing HIV transmission although its effectiveness in sexual abuse cases is not known.

o        The common side effects of the drugs should be explained (tiredness, nausea, diarrhoea and flu-like symptoms).  These are temporary, vary in intensity and do not cause long-term harm.        

o        The side effects of antiretroviral drugs may be aggravated when taken with other medication such as antibiotics.

o        The importance of compliance should be emphasised.

Parents/guardians of children presenting after 72 hours should be counselled about the possible risk of transmission and be given a follow-up appointment date for 6 weeks and 3 months for HIV testing and counselling.  If parents/guardians request antiretroviral prophylaxis, it should be explained that there is good evidence that the use of prophylactic drugs more than 72 hours following sexual abuse will have NO impact on preventing HIV transmission.

 

  1. HIV TESTING:

2.1.      Informed consent should always be obtained before HIV testing is done. Rapid testing should be made available where feasible and offered to patients when parents/guardians request it.  Where not feasible, blood should be drawn for routine laboratory HIV testing and a date given to the parent/guardian for follow-up.

2.2.      If the parent/guardian does not want immediate HIV testing of the child (either rapid or routine testing), this issue can be re-addressed at the first follow-up visit (within one week).

2.3.      If a child is already HIV-infected at the time of presentation, the child should be appropriately referred for long-term management.

2.4.      Post-exposure prophylaxis should start immediately. Do not wait for HIV test results unless immediately available.

 

3.        ANTIRETROVIRAL PROPHYLAXIS:

                                                                                                                                                                               

3.1.      Antiretroviral dosages: 3-drug prophylaxis is now the rule rather than the exception. AZT (zidovudine), 3TC (lamivudine) and Kaletra (a combination of 2 protease inhibitors – lopinavir/ritonavir) is recommended. In low-risk cases AZT and 3TC should be sufficient.

3.1.1 The dose for AZT (zidovudine) in children is 180 mg per meter square of body surface area 12 hourly for a period of 28 days.
A nomogram is attached to determine body surface area. Draw a straight line between the weight of the child marked on the weight scale and the child’s length/height on the height scale. Where the line crosses the surface area scale is the BSA of that child. To determine the dose, multiply the dose per meter square with the BSA.
Body surface area can be calculated as follows: Square root (child’s weight (kg) X length/height (cm) divided by 3600) = BSA

AZT is available in 100mg capsules and 10mg/ml suspension.

3.1.2 The dose of 3TC (lamivudine) is 4 mg/kg/dose 12 hourly. Lamivudine is available in 150 mg tablets, which can be broken, and a syrup containing 10mg/ml.

3.1.3 In older children with a weight of more than 35 kg, Combivir tablets (300 mg AZT + 150 mg 3TC) a combination of AZT and 3TC may be used. These tablets should not be broken in half, as the drugs are not evenly spread throughout the tablet.

3.1.4 The dose of Kaletra is calculated by child’s body weight according to the lopinavir dose as follows:
7-15 kg = 12 mg/kg 12-hourly
15-40 kg = 10 mg/kg 12-hourly
>40 kg = 400 mg 12-hourly with food (3 capsules)

Kaletra solution contains 80 mg/ml of lopinavir and capsules contain 133 mg lopinavir each.

3.2.      The following should be taken into consideration:

o  Children covered by a Medical Aid should be given a 3-day supply of the drugs and a prescription for the remaining 25 days.

o  Children who are not covered by a Medical Aid should be given a one-week supply of AZT, 3TC and Kaletra, and a date to return for reassessment within one week.

3.3.      All children should be seen after one week for follow-up assessment to obtain results of all tests.  The remainder of the antiretroviral drugs should be given at this visit (that is a 3-week supply).

3.4.      Subsequent follow-up visits should be at 6 weeks, 3 months and 6 months respectively for HIV and other relevant tests.

3.5.      Children who are known to be HIV-infected should not be offered antiretroviral prophylaxis.  They should be counselled and referred to an appropriate health facility for long-term management of their HIV status.

3.6.      Routine full blood count and liver enzymes for patients on antiretroviral prophylaxis only is not recommended.  Any blood tests should be performed according to the child’s symptoms and only if indicated by the clinical condition of the patient.

3.7.      Relative contra-indicators to the use of AZT include significant renal or liver impairment.  Where in doubt about the use of antiretroviral drugs in individual patients, contact your local physician or referral centre for advice.                  

 

e)       How would you further follow-up this child? (5)

First visit – one week: Results of special investigations, any development of further symptoms or improvement
Correct/adjust treatment according to results
Is the child safe – no further incidents (even if the child is removed from parents’ care)
Follow-up HIV/RPR tests (6weeks/3 months at least)
If psychosomatic type symptoms, evaluate for referral to mental health team
See that team is in place (Social worker etc)

 

f)         You are subpoenaed to appear in court regarding this case two years later. How would you prepare yourself for such a court appearance? (5)

Contact the state prosecutor and make necessary arrangements about time and place or where you could be contacted to appear on that specific day
Find and read your notes/J88 form/affidavit
Make sure that you have all the results available (special investigations) and notes on follow-up of the patient
Consult with expert if you are unsure how you should interpret certain findings and be sure of your facts
Dress conservatively, be on time

 

 

 

Paper 2 Question 4:

 

 A 14 month old baby boy is brought into the hospital by his mother. He is usually looked after by his grandmother in the Eastern Cape but has been brought to Cape Town because he is weak and there has been body swelling for a few days. On examination he is apathetic, miserable with generalized oedema, a diffuse rash including a severe nappy rash, and he has brittle hair.

 

a) What is the diagnosis?                                                                                                                   (2)

b) Describe your initial management of the child, indicating what specific complications you are looking for                                                                                                                                                   (12)

c) There is a high incidence of associated infections with this condition. What type of infections would you expect and what investigations would you do to try to diagnose them (minimum 4 infections and 4 investigations)                                                                                               (8)

d) Describe your subsequent approach to management once the patient has been stabilised              (12)

e) If this child’s mother decides to keep the child in Cape Town in the future, but she is unemployed and unmarried, what social support measure would the family be eligible for. What are the eligibility criteria, requirements and procedure for obtaining these            (6)

 

Answers:

1.

a) Kwashiorkor

 

b)

·         Resuscitate( Ringers/normal saline)

  • Diagnose/Manage Hypoglycaemia( 10%dextrose po/NG/iv, small frequent feeds)
  • Diagnose/Manage Hypothermia
  • Rehydrate (preferably orally)
  • Diagnose and correct electrolyte abnormalities especially hypokalaemia
  • Investigate and treat empirically for infection
  • Investigations including; FBC, Blood culture, electrolytes, Mg and Pi, stool culture etc
  • Then once stable: further history re feeding , TBContacts, diarrhea etc. Full examination including plotting growth parameters

 

c)                             Infections (4)                                         Investigations (4)

        Septicaemia esp gram -        Blood culture

        UTI                                                         urine MC&S

        Diarrhoea                                               stool MC&S

        Giardiasis                                               stool MC&S

TB                                                           Mantoux

                                                                Gastric washings

                                                                CXR

HIV                                                         HIV ELISA with appropriate councelling

Measles

Worm infestation

d)

  • Admit/inpatient management
  • Micronutrient supplementation  including vitamin A, zinc, potassium, Multivits, Mg and Pi(depending on results), folate
  • Treat infections: bacterial(ampi/genta, cephalosporin, amoxil or bactrim), giardia(flagyl), deworm(albendazole),
  • Initial refeeding: slow, small frequent feeds, no solids initially, rest sorol
  • Catchup growth watching for refeeding syndrome
  • Sensory stimulation and emotional support/play
  • Social work assessment/intervention/preparation for discharge and followup
  • Referral to PEM scheme

 

e)

  • Child support grant, R170 per month. Needs birth certificate of child, mother’s ID and proof of. no income/means test(<R9600/year in urban area, <R13 200 in rural area. Obtained through local social service
  • Also qualifies for PEM scheme  - referral by dietician or doctor.
  •  Maintenance from dad through court

 

 

Paper 2; Question 5:

 

a. What do you understand by the terms:

 

i)                    Dependency ratio?

 

Ratio of dependent population (those under 15 and over 64

                                years of age) to the working aged population (aged 15 – 64).

 

ii)                  Perinatal mortality rate?

 

Annual number of deaths from 28 weeks gestation to 7 days of

life per thousand total births.

 

iii)                Infant mortality rate?

 

Annual number of deaths of children under one year of age per

thousand live births.

 

iv)                  Under 5 mortality rate?

 

Annual number of deaths of children under five years of age per

thousand live births.

 

 

b. In this district what, if any, factors could contribute to the above mortality rates?           

 

Poor services

Overcrowding

Poverty

HIV

Unemployment

Inadequate health facilities

 

 

c. What are the five most likely diseases contributing towards the U5MR?          

 

GE

ARI

Malnutrition

HIV

Septicaemia

 

d. What steps would you take to reduce the PNMR?   

 

Antenatal

Spacing

Booking

Screening

Supplements

PEP training

Facilities

Referral systems & transport

 

Intrapartum

Monitoring

Resuscitation

 

Postnatal

Facilities

Protocols               To provide oxygen, warmth & energy

 

 

e. What would you do to reduce the U5MR?

 

GOBI FFF

Infrastructural development (WHS – water, housing & sanitation)

Job creation

Facts for life

Effective case management

IMCI

Vit A supplements

Clinical guidelines & protocols

pMTCT

ART

Integrated Nutrition Programme

 

 

f. What is a baby friendly hospital and what steps do you need to introduce to be accredited as such?             

 

A hospital that is accredited by UNICEF as meeting best practice standards to support & promote breastfeeding.

 

Standards are:

  1. Written breastfeeding policy
  2. Train staff in skills to implement the policy
  3. Inform pregnant women about benefits & management of breastfeeding
  4. Help mothers to initiate breastfeeding
  5. Show mothers how to initiate & maintain lactation
  6. Give newborn infants no food or drink other than breast milk unless medically indicated
  7. Practice rooming in
  8. Encourage breastfeeding on demand
  9. Give no artificial teats / pacifiers to breastfeeding infants
  10. foster the establishment of breastfeeding support groups

 

 

g. What is IMCI and provide a brief outline of its components?         

 

A strategy developed by the World Health Organization to reduce morbidity & mortality from the 5 most common conditions in infancy as well as HIV.

 

IMCI consists of three components:

 

Standard treatment guidelines (STGs)

                     i.             First step is a triage process i.e.

o        looking for General Danger Signs

o        Common approach – Ask, Check, Classify

o        Check for malnutrition & anaemia

o        Check immunization status

                   ii.             Treatment based on classification rather than diagnoses

o        Colour-coded algorithms

o        Follow up

                  iii.             Counsel mother

o        When to return

o        About food, feeding & fluids

o        About her own health

                 iv.             Training followed by supervision on site

 

Household and Community Component

                     i.             Aims to establish 15 key family practices

                   ii.             These cover issues such as breastfeeding, immunizations, disease prevention, early and appropriate treatment of common conditions e.g. use of ORS, improved health-care seeking practices

                  iii.             Also aims to improve the relationship and communication between primary health care facilities and local community

                 iv.             No single approach but includes identifying local resources and potential community partners

                   v.             Multisectoral approach – should include participation of other non-health sectors e.g. water and sanitation, social welfare, transport – to increase feasibility of achieving key family practices

 

Health Systems Review

                     i.             Aims to improve the infrastructure of health systems so as to enable primary care practitioners to effectively conduct their work

                   ii.             Includes national, provincial and local activities

                  iii.             Links with Essential Drugs List re. availability and dispensing of drugs

 

 

h. How would you monitor and evaluate the impact of the above actions?

 

Monitor basic health indicators – attendance, admissions, outcome – mortality rates (PNMR, IMR, U5MR), immunization rates etc

Quality assurance programmes – clinical audits, mortality reviews